- Описание
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Product Information
Description
ALDH6A1 rabbit polyclonal
Protein full name
Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
Synonyms
ALDH6A1, MMSADHA, MMSDH, Malonate-semialdehyde dehydrogenase [acylating], Aldehyde dehydrogenase family 6 member A1
Immunogen
KLH conjugated Synthetic peptide
corresponding to Mouse ALDH6A1
Isotype
IgG
Purity
Affinity purification
Predicted MW.
58 kDa
Observed MW.
58kDa
Uniprot ID
Applications
Applications
Species
Dilution
Positive Tissue
WB
Mouse, Rat
1:300-1:1000
liver, kidney
Background
This gene encodes a member of the aldehyde dehydrogenase protein family. The encoded protein is a mitochondrial methylmalonate semialdehyde dehydrogenase that plays a role in the valine and pyrimidine catabolic pathways. This protein catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids. Alternate splicing results in multiple transcript variants.
Images

Western blot analysis of ALDH6A1 (GB113786) at dilution of 1: 1000 Storage
Storage Store at -20 ℃ for one year. Avoid repeated freeze/thaw cycles. Storage Buffer PBS with 0.02%sodium azide,100 μg/ml BSA and 50% glycerol. NOTE:
1.This product is intended for research only.
2.This product is recommended to dilute with the Primary Antibody Dilution Buffer (G2025).







